[A case of extensive macular atrophy and pseudodrusen-like appearance].

نویسندگان

  • M Govare
  • C Seguy
  • M-B Rougier
  • M-N Delyfer
  • J-F Korobelnik
چکیده

In 2009, Hamel et al. [1] proposed the disease “extensive macular atrophy with pseudodrusen-like appearance” (EMAP) as a new clinical entity. It is characterized by early-onset (<50 years) bilaterally symmetric macular atrophy with increased vertical axis, surrounded by numerous pseudodrusen-like deposits, with rapid involvement of the fovea and entire posterior pole. In addition, EMAP patients have presented with paving-stone degeneration predominantly in the inferior part of the peripheral retina. To our knowledge, there are two reports in the literature describing EMAP [1,2]. Furthermore, there is one report describing the optical coherence tomography (OCT) findings in EMAP patients [1]. Herein, we report a single case of EMAP.

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عنوان ژورنال:
  • Journal francais d'ophtalmologie

دوره 39 8  شماره 

صفحات  -

تاریخ انتشار 2016